Takagi H, Matsunami K, Imai A
J Obstet Gynaecol 2010 May;30(4):350-3
PMID: 20455715
ヒトにおけるミューラー管の融合不全はHerlyn-Werner-Wunderlich syndromeと呼ばれている。膣に及ぶ重複にとどまらず、腎系の低形成を伴うことが多い。重複した膣は盲端になり、月経時の出血が貯留することから、周期的な腰痛という稟告で発見されることが多い。
Abstract
Congenital abnormalities of the Müllerian duct system can result in various urogenital anomalies, including uterus didelphys with blind hemivagina and ipsilateral renal agenesis (Herlyn-Werner-Wunderlich syndrome). It usually presents after the menarche with progressive pelvic pain during periods secondary to haematocolpos. However, rarely presentation is unusual with consequent diagnostic delay. This paper attempts to review the medical literature for rare presentations that make diagnosis and treatment difficult, including our cases. Clinicians must be aware of the importance of this rare congenital anomaly of the female genital tract, especially many years after the menarche. This condition should be considered to prevent misdiagnosis or suboptimal treatment.